OBJECTIVE: Paroxysmal nocturnal hemoglobinuria ( PNH ) is an acquired disease of the pluripotent hematopoitec stem cell.

[目的]阵发性睡眠性血红蛋白尿症 ( PNH ) 系后天获得性干细胞克隆性异常,临床表现为间断溶血、静脉血栓及不同程度的骨髓衰竭.

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Objective : To study the effect of T - lymphocytes on hematopoietic progenitors in patients with paroxysmal hemoglobinuria ( PNH ).

目的: 研究阵发性睡眠性血红蛋白尿症 ( PNH ) 患者的 T 淋巴细胞对造血祖细胞的影响.

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Soliris acts to block the complement system activity, including the destruction of PNH red blood cells.

它的机制主要通过抑制血液中补体系统的活性, 从而使发育异常的红细胞免遭破坏.

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